INFANTILE CRONKHITE-CANADA SYNDROME - CASE-REPORT


Küçükaydın M., Patıroğlu T. E. , OKUR H., İçer M.

EUROPEAN JOURNAL OF PEDIATRIC SURGERY, cilt.2, ss.295-297, 1992 (SCI İndekslerine Giren Dergi) identifier

  • Cilt numarası: 2 Konu: 5
  • Basım Tarihi: 1992
  • Doi Numarası: 10.1055/s-2008-1063463
  • Dergi Adı: EUROPEAN JOURNAL OF PEDIATRIC SURGERY
  • Sayfa Sayısı: ss.295-297

Özet

This is a case report of juvenile gastrointestinal polyposis involving the gastrointestinal system from the stomach to the rectum. Only few cases have been reported and extra-intestinal manifestations of this syndrome include macrocephaly, hepatosplenomegaly, hypotonia, clubbing of fingers, anemia and protein-losing enteropathy. The disease usually has a poor prognosis, and the children rarely live more than 2 years.