JOURNAL OF THE NATIONAL MEDICAL ASSOCIATION, vol.102, no.3, pp.247-249, 2010 (Peer-Reviewed Journal)
We report a patient with medullary sponge kidney (MSK) who presented with hematuria and nephrotic-range proteinuria. Renal biopsy revealed a diagnosis of renal AA amy loidosis. No secondary factors contributing to renal amyloidosis were demonstrated. To the best of our knowledge, this is the first reported case that demonstrates the coexistence of MSK and renal AA amyloidosis.